Cardiopulmonary exercise testing reveals onset of disease and response to treatment in a case of heritable pulmonary arterial hypertension
نویسندگان
چکیده
Patients affected by pulmonary arterial hypertension (PAH) show a typical pattern of abnormalities on cardiopulmonary exercise testing (CPET). However, CPET is not routinely used as a screening method. We discuss a patient with hereditary PAH in whom CPET revealed onset of disease. Furthermore, we show that the abnormalities observed can improve in part by PAH-specific treatment.
منابع مشابه
Should cardiopulmonary exercise testing become a part of regular evaluation for patients with a family history of pulmonary hypertension? Regarding “Cardiopulmonary exercise testing reveals onset of disease and response to treatment in a case of heritable pulmonary arterial hypertension”
The prognostic implications of CPET responses in patients with PH are beginning to gain recognition. For the CPET variables reported by Trip et al.,[1] we have provided the survival rates based on cut-off values from previous studies. An oxygen consumption (VO2) <1.32 l/kg/min has cumulative survival rates of 71%[5] and an oxygen (O2) pulse <12 ml/beat with and without cardiopulmonary disease h...
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